Cystic Fibrosis Quiz

Quiz Questions for Cystic Fibrosis

1. Which of the following is a multisystem generic disorder that is noted for its chronic obstructive pulmonary disease, GI disturbances, and exocrine dysfunction? A. Celiac Disease B. Kawasaki Disease C. Cystic Fibrosis D. Pneumonia

Correct answer: C
Cystic fibrosis (CF) a multisystem illness that can vary in how severe it is. The illness causes the respiratory epithelium to exhibit marked impermeability to chloride and excessive sodium reabsorption. The lung tissue become inflamed with chronic infection shortly after birth. Mucus becomes viscous, and dehydration of the airway secretions occurs, leading to dysfunctional mucociliary transport, airway obstruction, and chronic infections (Burns, Dunn, Brady, Barber Starr, & Blosser, 2009, p. 829). Eighty-five percent of affected children have failure to thrive due to pancreatic enzyme insufficiency, and diet is a very important component of treatment. CF patients have a 30% chance of having endocrine issues by adulthood. It is essential that blood glucose levels are obtained at least every year (Burns et al., 2009, p. 831).

2. What is the gold standard for diagnosing cystic fibrosis? A. Lung volumes B. Sweat test C. Spirometry D. Bronchodilator response testing

Correct …show more content…
The sweat test is called the pilocarpine iontophoresis sweat test. The test measures the concentration of chloride in sweat after the patient is stimulated with pilocarpine. There are specific guidelines for collection and analysis. A test is considered intermediate if the result is 30 to 59 mmol/L for infants younger than six months or 40 to 59 mmol/L for older individuals. Results that are consistent with cystic fibrosis are those >60 mmol/L (Burns et al., 2009, p. 830). Some conditions can elicit a false-negative test test such as a child with hypoproteinemia. (Burns et al., 2009, p.

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