Cystic Fibrosis Case Study

Words: 637
Pages: 3
Open Document
Matthew is a 14-year-old boy with Cystic Fibrosis (CF) diagnosed at birth. The priority problems of Matthew are chronic chest infection and potential nutritional deficiency. The two interventions for chest infection include antibiotics treatment and chest physiotherapy. The interventions for malnutrition are to manage his noncompliance with medication and educate on the importance of treatment. The aim of this case study is to relieve those lifelong issues in CF with appropriate interventions and to promote the patient’s lung function and healthy nutritional status, that ultimately support him to manage the chronic conditions in his everyday life.

The first priority problem of Matthew is chronic chest infection, the main clinical feature …show more content…
It mainly controls the chloride and bicarbonate channel but also acts on epithelium sodium channel (Lobo, Rojas-Balcazar, & Noone, 2012, p.311). The loss of CFTR function decreases the chloride secretion and increases the sodium absorption (Spielberg & Clancy, 2016, p.157), which causes dehydrated mucus and reduced airway surface liquid on bronchus (Gilligan, 2014, p.198). Consequently, this impairs mucociliary clearance and allows the environment to be susceptive to inflammation and infection (Spielberg …show more content…
In Matthew’s case, he is prescribed tobramycin 300mg via inhalation twice a day. Tobramycin, an aminoglycoside, is commonly used in CF as it discourages the protein synthesis of Pseudomonas aeruginosa bacteria, the most targeted pathogen in CF (Maselli, Keyt, & Restrepo, 2017, p.3-4; Molloy & Nichols, 2015, p.569; Spielberg & Clancy, 2016, p.160). It resolves the bacterial infection in the lower airways and improves lung function, thus reducing rates of exacerbations (Maselli et al., 2017, p.4). The common side effects of tobramycin are cough, altered voice and tinnitus which should be observed carefully because of the potential risk of cochlear toxicity (Maselli et al., 2017, p.5; Sommerwerck et al., 2014, p.1794). As a collaborative intervention, nurses play a crucial role in administering medication and educating patients and carers about medication (Shone, Yin, & Wolf, as cited in Gibson, Stelter, Haglund, & Lerret, 2017, p.226), including regimes, signs of side effects and interactions (Yetzer, Goetsch, & St. Paul, 2011, p.257). In regards to administering, nurses are responsible for correct medication, thus required to adhere to seven rights (right patient, drug, time, dose, route, reason and documentation) before administration (Smeulers et al., 2015, p.2-3). Also, especially in cases such as
Show More

Related Documents: Cystic Fibrosis Case Study

Cystic Fibrosis Hospital Case Study

guests are patients with Cystic Fibrosis and the thirteenth floor of Barnes Jewish Hospital has been like a home to them for years. Dedicated to patients with Cystic Fibrosis, life on patient division 1300 is different from other floors in the hospital. Having the luxury of calling this floor home for a prescribed period of time has its perks as these patients…

Words 875 - Pages 4

Cystic Fibrosis Research Paper

Cystic Fibrosis: The Lungs’ Worst Enemy Ayde Blanco, Noelia Ezquivel, Hannah Jiao, Elaine Proa Texas A&M International University Abstract Cystic Fibrosis, a recessively genetic received disease, is a dangerous lung defect that occurs in almost 200,000 people each year. It is only inherited and works by damaging the lungs and the digestive system. It hazardously affects cells that create mucus, sweat, and digestive juices inside of your body. While these fluids are meant to act as a…

Words 1551 - Pages 7

Pseudomonas Aeruginosa Research Paper

Pseudomonas Aeruginosa is a gram negative rod-shaped bacterium that can cause disease in both plants and animals. It is resistant to antibiotics. Is considered an opportunistic bacteria causing cystic fibrosis. Pseudomonas Aeruginosa has a flagella and are motile. P. aeruginosa is not a fermenter of carbohydrates and has an optimal growth in aerobic atmosphere even through it will still grow slowly in an anaerobic environment if nitrate is present as the hydrogen acceptor. Pseudomonas Aeruginosa…

Words 1675 - Pages 7

Pharmacogenomics CF Essay

Pharmacogenomics of Cystic Fibrosis Cystic Fibrosis (CF) is the most common lethal inherited disease among whites, affecting approximately 70,000 people worldwide.1 It is an autosomal recessive disease, and the defective gene involved is the cystic fibrosis transmembrane conductance regulator (CFTR) gene that codes for the CFTR protein. This is an epithelial ion channel that has a role in regulating the absorption and secretion of chloride ions across cell membranes in the lungs, pancreas and…

Words 1139 - Pages 5

Essay about Vertex Pharmaceuticals FINAL Nov 26

Second HIV protease inhibitor co-developed by GlaxoSmithKline was approved by the FDA. June 2006: Vertex signed a collaboration with Johnson and Johnson on Hepatitis C. 2007: Vertex conducted clinical development of oral medicines targeting cystic fibrosis. Nov 2010: Vertex completed its first New Drug Application to the FDA (IncivekTM). May 2011: IncivekTM, Vertex’s first medicine was approved by the FDA. Jan 2012: Vertex received FDA approval for its second medicine, KalydecoTM. Oct 2013: R&D…

Words 4515 - Pages 19

Rectal Prolapse Research Paper

of the rectal mucosa to the underlying muscularis, and the absence of Houston valves in about 75% of infants. Although cystic fibrosis is not a likely diagnosis in patients who present with rectal prolapse, a sweat test is indicated in all patients who present without an underlying anatomic abnormality. Rectal prolapse occurs in 20% of patients with cystic fibrosis who are aged 6 months to 3 years. Most prolapses get spontaneously reduced. Failure to reduce may lead to venous stasis, edema…

Words 2706 - Pages 11

Essay about Case assignment

NURS 315 Pathophysiology Module 1 Genetics Case Study Name _____Tammy Bills_______________________________________________ Review the following case study and answer the questions for each part located at the end of the case. Submit as directed to the drop box. “In Sickness and in Health” by Barry Chess Page A Trip to the Genetic Counselor Part 1—Pedigree Construction Greg and Olga were both a little worried. Starting a family presented choices and responsibilities far more long-reaching…

Words 2934 - Pages 12

Essay Orem's Theory

Predictors of Self-Care in Adolescents With Cystic Fibrosis: A Test of Orem's Theories of Self-Care and Self-Care Deficit Lois K. Baker, PhD, RN, CPNP Mary J. Denyes, PhD, RN, FAAN Pediatric nurses often struggle to find ways to encourage adolescents with cystic fibrosis (CF) to engage in self-care that is essential to their health and life. A study of predictors of self-care was conducted to provide a stronger evidence base for nursing practice with these youth. Orem's theories of self-care…

Words 7700 - Pages 31

Essay about Geneticist Carrear Journal Copy

interact with genetic counselors. Often times they will evaluate patients at risk for inherited diseases, like Alzheimer's, and treat inherited disorders such as cystic fibrosis, hemophilia and sickle cell disease. They also treat different forms of cancer and other abnormal conditions associated with genetics. They usually begin a case by analyzing the medical history of their patient and the family of the patient. They then take some DNA from the patient using a system called gel electrophoresis…

Words 547 - Pages 3

Research Paper On Aspergillus

so that is why he named the genus likewise. Scientists intentionally browsed different nations and mainlands have added to this uncommon issue managing all the medicinal parts of IA, including scientific categorization, hereditary qualities, the study of disease transmission, pathogenesis, antifungal resistance, and novel remedial viewpoints. Numerous species have now been distinguished inside the Aspergillus segment Fumigati and the conceivable relationship between their metabolite profiles and…

Words 1801 - Pages 8